11歳児の肩に発生した孤立性結節。

Solitary nodule on the shoulder of an 11-year-old child.

• Mariana Esteves
• Sofia Lopes
• Maria João Cruz
• Filomena Azevedo
• Alberto Mota

抄録

叢状線維組織細胞性腫瘍は中悪性度の珍しい軟部組織新生物であり、最も頻繁に無痛性でゆっくりと成長する結節として発生し、小児および若年成人に明確な好発性を示す。我々は健康な11歳の少年で、左肩に無症候性の皮膚結節を1年前から認めた。病理組織学的および免疫組織化学的検査の結果、lexiform fibrohistiocytic tumorと診断された。通常良性の臨床経過をたどるにもかかわらず、この新生物は頻繁な局所再発と時折の転移を起こしやすい。小児患者における拡大結節の鑑別診断において考慮すべきである。

Plexiform fibrohistiocytic tumor is an uncommon soft tissue neoplasm of intermediate malignancy, most frequently occurring as a painless, slow-growing nodule that shows a distinct predilection for children and young adults. We report a healthy 11-year-old boy presenting with a 1-year history of an asymptomatic cutaneous nodule on his left shoulder. Histopathological and immunohistochemical analysis confirmed a diagnosis of plexiform fibrohistiocytic tumor. Despite following a usually benign clinical course, this neoplasm is prone to frequent local recurrence and occasional metastatic ability. It should be considered in the differential diagnosis of an enlarging nodule in pediatric patients.