Cleidocranial dysplasiaのケースシリーズ。萌出遅延永久歯のX線写真による追跡調査

Case series of cleidocranial dysplasia: Radiographic follow-up study of delayed eruption of impacted permanent teeth.

• Han-Gyeol Yeom
• Won-Jong Park
• Eun Joo Choi
• Kyung-Hwa Kang
• Byung-Do Lee

抄録

この報告では，頭蓋裂溝形成不全症（CCD）の3症例を取り上げ，萌出遅延を伴う永久歯衝突部のX線画像の長期追跡調査で得られた関連所見を紹介する。3名のCCD患者のX線画像をレトロスペクティブに検討した．これらの画像は，主にパノラマと頭蓋骨のX線写真で構成されており，追跡期間はそれぞれ3年，13年，13年であった．これらの画像から明らかになった特徴を説明し，衝突永久歯の萌出状態を評価した．3例に共通した特徴は，複数の上顎歯，Wormian boneの存在，上顎と上顎洞の未発達，鎖骨低形成であった．成人のCCD症例では、適切な歯科治療を行わなければ、長期間経過してもインパクトのある永久歯の萌出は認められませんでした。適切な矯正力を加えれば、一般人と有意差のない歯の移動が認められた。

This report describes 3 cases of cleidocranial dysplasia (CCD) and presents relevant findings on long-term follow-up radiographic images of impacted permanent teeth with delayed eruption. Radiographic images of 3 CCD patients were reviewed retrospectively. These images were mainly composed of panoramic and skull radiographs, and the follow-up periods were 3, 13, and 13 years, respectively. The distinct features revealed by the images were described, and the eruption state of impacted permanent teeth was evaluated. The features common to the 3 cases were multiple supernumerary teeth, the presence of Wormian bone, underdevelopment of the maxilla and the maxillary sinus, and clavicular hypoplasia. The eruption of impacted permanent teeth was not observed without proper dental treatment in adult CCD cases, even after long time periods had elapsed. When proper orthodontic force was applied, tooth movement was observed in a manner not significantly different from the general population.

Copyright © 2019 by Korean Academy of Oral and Maxillofacial Radiology.