急速に侵襲する先天性血管腫と壊死性筋膜炎の遅発性合併症の特徴が重なるカポシ状血管内皮腫

Kaposiform hemangioendothelioma with overlapping features of rapidly involuting congenital hemangioma and a delayed complication of necrotizing fasciitis.

• Lina Belmesk
• Josée Dubois
• Louise Caouette-Laberge
• Michèle David
• Patricia Bortoluzzi
• Victor Kokta
• Afshin Hatami
• Catherine C McCuaig

抄録

急速に侵襲する先天性血管腫と遅発性の壊死性筋膜炎を合併した。我々の症例は、急速に侵襲する先天性血管腫によく見られる皮下萎縮と突出した静脈を残して侵襲した珍しい症例であった。年齢の3歳で、子供はKHEが退行していた領域に限局した再発表在性血栓性静脈炎を開発しました。その後、彼は同じ場所に壊死性筋膜炎と血栓性静脈とグループA溶連菌性敗血症性ショックを開発しました。

We report the case of a male infant born at term with kaposiform hemangioendothelioma (KHE) of the right forearm and coagulopathy. Our case was unusual as it involuted leaving subcutaneous atrophy and prominent veins, which are more commonly observed in rapidly involuting congenital hemangioma. At 3 years of age, the child developed recurrent superficial thrombophlebitis localized to the area where the KHE had regressed. Subsequently, he developed necrotizing fasciitis and thrombotic veins in the same location and group A streptococcal septic shock.

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