血友病患者における手の筋骨格系の問題

Musculo-skeletal problems of the hand in haemophilia.

• Elena Bravo
• Raul Barco
• E Carlos Rodríguez-Merchán

抄録

血友病患者における手の筋骨格系の合併症はまれであり、滑膜炎、関節症、仮性腫瘍、手根管症候群、血管瘤や仮性動脈瘤などがあります。これらの患者の治療は、血液内科医と手外科医の間の緊密な連携を持つ施設で行われるべきである（すべての外科的処置は、常に欠損凝固因子のカバーの下で実行されなければならない）。この記事を引用します。 2020;5:328-333.DOI: 10.1302/2058-5241.5.190078.

Musculo-skeletal complications of the hand in the haemophilia patient are rare, and they include synovitis, arthropathy, pseudotumours, carpal tunnel syndrome and vascular aneurysms and pseudoaneurysms.The best way to prevent the aforementioned musculo-skeletal complications is early continuous haematological primary prophylaxis (intravenous infusion of the deficient coagulation factor, ideally from cradle to death).There is a wide range of procedures that a hand surgeon treating these patients should be able to manage, including synovectomy, prosthetic replacement of small joints, removal or curettage of pseudotumours, release of carpal tunnel and, occasionally, vascular reconstruction of aneurysms.The treatment of these patients should be made at an institution with close collaboration between haematologists and hand surgeons (all surgical procedures must always be performed under cover of the deficient coagulation factor). Cite this article: 2020;5:328-333. DOI: 10.1302/2058-5241.5.190078.

© 2020 The author(s).